MSUD product journey

Please note:

  • All of the products below are Foods for Special Medical Purposes and must be used under medical supervision.
  • Availability of products vary from country to country. Please contact your healthcare professional or local Nutricia contact for more information which products are available in your region.

MSUD Product Journey

When an infant is diagnosed with maple syrup urine disease (MSUD), Anamix infant is the first introduction to the nutritional solutions provided by Nutricia Metabolics. 

At every stage in life, we are there with products and services to support the dietary management of MSUD.

MSUD Anamix Infant

MSUD Anamix infant

MSUD Anamix infant contains an optimal composition of amino acids and other macro/micronutrients, which meet the nutritional needs of infants with metabolic disorders from day one and for every milestone ahead.

For use in infants from birth to 12 months and as a supplementary feed up to 3 years.

For use in the dietary management of proven Maple Syrup Urine Disease. It is an amino acid-based isoleucine-free, leucine-free, valine-free, powdered mixture containing essential and non-essential amino acids, carbohydrate, fat, fibre, vitamins, minerals and trace elements.

  • Only infant feed for metabolic conditions that contains the prebiotic fibre blend scGOS:lcFOS(9:1)*1
  • Convenient and easy to use
  • Developed to comply with the highest quality and food safety standards**
  • Available in a 400g can

Ingredients: Glucose syrup, vegetable oils (high oleic sunflower oil, coconut oil, rapeseed oil, sunflower oil), galacto-oligosaccharides (from cow's milk), L-lysine-L-glutamate, L-proline, L-arginine, glycine, L-aspartic acid, L-threonine, emulsifier (citric acid esters of mono- and diglycerides of fatty acids), L-phenylalanine, L-tyrosine, L-serine, calcium phosphate, L-histidine, L-alanine, potassium citrate, L-cystine, fructo-oligosaccharides, potassium chloride, L-tryptophan, choline bitartrate, magnesium acetate, L-methionine, calcium glycerophosphate, sodium hydrogen phosphate, oil from Crypthecodinium cohnii, oil from Mortierella alpina, sodium chloride, L-glutamine, inositol, L-glutamic acid, L-ascorbic acid, antioxidants (sunflower lecithin, ascorbyl palmitate), taurine, ferrous sulphate, zinc sulphate, L-carnitine, DL-α tocopheryl acetate, calcium D-pantothenate, nicotinamide, copper sulphate, thiamin hydrochloride, pyridoxine hydrochloride, riboflavin, retinyl acetate, potassium iodide, manganese sulphate, pteroylmonoglutamic acid, chromium chloride, phytomenadione, sodium selenite, sodium molybdate, D-biotin, cholecalciferol, cyanocobalamin.
Allergens: Cow’s milk

As a child grows their nutritional needs also change

MSUD Anamix junior

Adapted to the changing needs of a growing child and designed to taste great.***

For use in children 1 to 10 years of age.

A leucine, isoleucine and valine free powder drink mix containing a balanced mix of the other essential and non-essential amino acids, carbohydrates, fat (including docosahexaenoic acid (DHA)), vitamins, minerals, trace elements and fibre.

  • The only protein substitute for 1 - 10 year olds with added fibre
  • Contains a unique fibre blend to support gut health2-7.
  • MSUD Anamix junior is available in neutral flavour to help transition from Anamix infant.
  • Available in a 400g can and convenient 36g sachets for on-the-go use.

Ingredients: Dried glucose syrup, dietary fibres (oligofructose, inulin, resistant starch, cellulose, arabic gum, soy polysaccharides), refined vegetable oils (high oleic sunflower, canola, medium chain triglycerides (palm kernel and/or coconut oil), sunflower), L-alanine, glycine, L-lysine acetate, L-glutamine, L-threonine, calcium phosphate di basic, L-tyrosine, L-proline, flavouring, L-phenylalanine, L-cystine, L-arginine, tri potassium citrate, tri sodium citrate, L-serine, calcium chloride, L-histidine, L-methionine, maltodextrin, choline bitartrate, magnesium hydrogen phosphate, L-tryptophan, emulsifiers (E472c, sunflower lecithin), magnesium L-aspartate, high docosahexaenoic acid oil from Crypthecodinium cohnii, L-asparagine, tri calcium citrate, L-ascorbic acid, M-inositol, taurine, ferrous sulphate, L-carnitine, zinc sulphate, DL-ɑ tocopheryl acetate, calcium D-pantothenate, manganese sulphate, nicotinamide, copper sulphate, thiamin hydrochloride, pyridoxine hydrochloride, riboflavin, vitamin A acetate, Antioxidants (E304(i), E306, E307), folic acid, potassium iodide, sodium molybdate, sodium selenite, chromium chloride, vitamin D3, vitamin K1, D-biotin, cyanocobalamin.
Allergens: Soy

MSUD Anamix Junior range
MSUD Anamix Junior LQ

MSUD Anamix junior LQ

An orange flavoured, ready to use protein substitute. Easy to take to nursery or school.

For use in children 1 to 10 years of age.

An isoleucine, leucine, and valine free drink, containing a balanced mix of the other essential and non-essential amino acids, carbohydrates, fat, vitamins, minerals, and trace elements. Contains docosahexaenoic acid (DHA).

  • Convenient and easy to use packaging.
  • Orange flavoured.
  • Available in 10g PE per 125ml resealable bottle.

Ingredients: Water, sugar, refined vegetable oil (high oleic sunflower, canola, walnut oil), flavouring, dried glucose syrup, L-lysine acetate, calcium glycerophosphate, L-proline, L-tyrosine, tri sodium citrate, L-arginine, glycine, tri potassium citrate, L-serine, L-aspartic acid, flavour enhancer (E330), L-alanine, L-threonine, L-cystine, L-phenylalanine, L-histidine, emulsifiers (E471, E472e, soy lecithin), calcium chloride, stabilisers (E460(i), E412, E415), magnesium acetate, taurine, N-acetyl L-methionine, L-tryptophan, L-ascorbic acid, high docosahexaenoic acid oil from Crypthecodinium cohnii, choline bitartrate, tri calcium citrate, L-carnitine, ferrous sulphate, zinc sulphate, M-inositol, artificial sweetener (sucralose), nicotinamide, DL-ɑ tocopheryl acetate, calcium-D-pantothenate, copper sulphate, manganese sulphate, pyridoxine hydrochloride, antioxidants (E304, E307), thiamine hydrochloride, riboflavin, vitamin A acetate, sodium selenite, potassium iodide, chromium chloride, folic acid, sodium molybdate, D-biotin, vitamin K1, vitamin D3, cyanocobalamin.
Allergens: Walnut, soy

Following on from MSUD Anamix, MSUD Lophlex is the next step for older children and adults

MSUD Lophlex

A low volume protein substitute, easy to use on the go

For use in children from 4 years of age, teenagers, and adult, including pregnant women (in conjunction with standard folic acid supplementation).

An isoleucine, leucine, and valine free drink, containing a balanced mix of the other essential and non-essential amino acids, vitamins, trace elements and minerals. Contains docosahexaenoic acid (DHA).

  • Only 99Kcal per 20g PE sachet
  • Contains DHA8-10, as the intake of this essential fatty acid may be low in protein-restricted diets11.
  • Available in 28g sachets in a neutral flavour.

Ingredients: L- glutamine, L-lysine acetate, L-proline, dried glucose syrup, L-tyrosine, L-arginine, glycine, L-serine, L-aspartic acid, L-alanine, calcium hydrogen phosphate, L-threonine, L-cystine, L-phenylalanine, L-histidine, magnesium acetate, flavouring, L-tryptophan, choline bitartrate, L-methionine, oil from Crypthecodinium cohnii, stabiliser (E412), modified starch (E1450), potassium citrate, flavour enhancer (E330), calcium phosphate, taurine, sodium L-ascorbate, high oleic sunflower oil, inositol, potassium phosphate monobasic, ferrous sulphate, zinc sulphate, L-carnitine, nicotinamide, DL-ɑ-tocopheryl acetate, artificial sweetener (sucralose), calcium D-pantothenate, copper sulphate, manganese sulphate, pyridoxine hydrochloride, thiamin hydrochloride, riboflavin, retinyl acetate, folic acid, potassium iodide, sodium molybdate, D-biotin, sodium selenite, chromium chloride, phytomenadione, cholecalciferol, cyanocobalamin.
Allergens: N/A

MSUD Lophlex
MSUD Lophlex LQ range

MSUD Lophlex LQ

Our lowest volume and lowest calorie liquid protein substitute

For use in children from 4 years of age, teenagers, and adult, including pregnant women (in conjunction with standard folic acid supplementation).

For the dietary management of proven maple syrup urine disease (MSUD), a leucine, isoleucine, and valine free amino acid-based liquid, containing vitamins, trace elements and some minerals, containing mixed fruit juices (from concentrate) and natural flavourings.

  • Only 60 Kcal in only 62.5 ml (10g PE) and 120 Kcal in only 125 ml (20g PE).
  • Contains DHA8-10, as the intake of this essential fatty acid may be low in protein restricted diets11.
  • Available in juicy berries flavour in a resealable pouch.

Ingredients: Water, apple juice from concentrate (34.1%), grape juice from concentrate (6.9%), blackcurrant juice from concentrate (2.5%), L-lysine acetate, L-proline, flavour enhancer (E330), L-tyrosine, L-arginine, glycine, L-serine, L-aspartic acid, L-alanine, L-threonine, dried glucose syrup, L-cystine, L-phenylalanine, dicalcium phosphate, L-histidine, elderberry juice from concentrate (0.6%), maltodextrin, magnesium acetate, N-acetyl-L-methionine, L-tryptophan, choline bitartrate, stabilisers (E460(i), E412, E415, E466), high docosahexaenoic acid oil from Crypthecodinium cohnii, sugar, natural flavouring, L-ascorbic acid, concentrates (apple, blackcurrant, radish), taurine, emulsifier (E322), artificial sweeteners (sucralose, acesulfame K), preservatives (E202, E211), M-inositol, ferrous lactate, zinc sulphate, L-carnitine nicotinamide, DL-alpha tocopheryl acetate, calcium D-pantothenate, manganese sulphate, copper sulphate, thiamin hydrochloride, pyridoxine hydrochloride, vitamin A palmitate, riboflavin, antioxidants (E304, E306), folic acid, potassium iodide, sodium molybdate, D-biotin, sodium selenite, chromium chloride, vitamin K1, vitamin D3, cyanocobalamin.
Allergens: N/A

Continue dietary management with MSUD MAXAMUM, an energy-dense protein substitute

MSUD Maxamum

MSUD Maxamum is an energy-dense protein substitute that can be concentrated.

Suitable for children from 8 years of age, teenagers, and adult, including pregnant women (in conjunction with standard folic acid supplementation).

  • High in energy and very low in fat protein substitute to meet more complex nutritional needs.
  • An isoleucine, leucine and valine-free powdered mixture of amino acids, carbohydrates, vitamins, minerals, and trace elements.
  • Available in two varieties: unflavoured and orange.
  • Available in a 500g can.

Ingredients: Dried glucose syrup, L-arginine, L-aspartate, L-lysine, L-glutamine, L-proline, glycine, calcium glycerophosphate, L-threonine, L-phenylalanine, L-tyrosine, L-serine, L-histidine, L-alanine, tri potassium citrate, L-cystine, N-acetyl L-Methionine, L-Tryptophan, magnesium hydrogen phosphate, sodium chloride, tri sodium citrate, sugar, choline bitartrate, emulsifier (soy lecithin), magnesium acetate, magnesium L-aspartate, taurine, ferrous sulphate, ascorbic acid, inositol, zinc sulphate, L-carnitine, nicotinamide, manganese sulphate, DL-α-tocopheryl acetate, calcium D-pantothenate, copper sulphate, pyridoxine hydrochloride, thiamin hydrochloride, riboflavin, vitamin A acetate, folic acid, chromium sulphate, sodium molybdate, potassium iodide, biotin, sodium hydrogen selenite, vitamin K1, vitamin D3, cyanocobalamin.
Allergens: Soy

MSUD Maxamum range

Other Essentials

We offer other essential products to personalise the dietary management of MSUD to meet specific daily nutritional requirements and as part of an individually tailored emergency regime.

MSUD Aid III

MSUD Aid III

A concentrated source of protein to meet extra requirements in all ages, which can be added to usual daily protein substitute or taken on its own.

Suitable for infants, children and adults.

For the dietary management of maple syrup urine disease (MSUD) and related conditions where it is necessary to limit the intake of branched chain amino acids. An isoleucine, leucine, and valine free powdered mixture of other essential and non-essential amino acids.

  • Mix with usual daily protein substitute or use on its own.
  • May be given in a concentrated form, e.g. a paste or concentrated drink. Can also be added to other low-protein drinks.
  • Available in a 500g can.

Ingredients: L-lysine L-glutamate, L-proline, L-arginine, glycine, L-aspartic acid, L-threonine, L-tyrosine, L-phenylalanine, L-serine, L-histidine, L-alanine, dried glucose syrup, L-cystine, L-tryptophan, L-methionine, L-glutamine, L-glutamic acid, tricalcium phosphate, taurine, L-carnitine.
Allergens: N/A

Super Soluble Maxijul

A powdered neutral-flavoured carbohydrate energy source.

Suitable for infants, children, and adults

A powdered carbohydrate energy supplement derived from the hydrolysis of corn starch to produce a glucose polymer of approximately five glucose units. Forms an integral part of a patient’s emergency regime whereby individual energy requirements can be dose matched.

  • Flexible to mix with existing protein substitutes, low-protein sweet or savoury foods and low-protein hot or cold drinks.
  • Available in 200g can

Ingredients: Dried glucose syrup
Allergens: N/A

Super Soluble Maxijul
Duocal Super Soluble

Super Soluble Duocal

A powder consisting only of a balanced blend of fats and carbohydrates.

Suitable for infants, children and adults.

A powder consisting of a balanced blend of fat and carbohydrate. Milk protein free. Can be used as part of a patients' emergency regime or to meet increased energy requirements in general.

  • Enables you to tailor to your patient's individual energy requirements.
  • Available in a 400g can.

Ingredients: Dried glucose syrup, medium chain triglycerides (palm kernel and/or coconut oil), safflower oil, canola oil, emulsifier (E472(c)).
Allergens: N/A

Energivit

For infants and children requiring additional energy and micronutrients on a protein-restricted diet.

Suitable for infants and children

For the dietary management of conditions where protein intake is restricted or where additional energy, vitamins, minerals and trace elements are required. A protein-free powdered mixture of carbohydrate, fat, vitamins, minerals, and trace elements.

Gives flexibility to cater to patient's individual energy, vitamins and minerals requirements.

  • Suitable for bottle, tube and sip feeding
  • Available in a 400g can

Ingredients: Glucose syrup, vegetable oils (high oleic sunflower oil, coconut oil, rapeseed oil, sunflower oil), emulsifier (citric acid esters of mono- and diglycerides of fatty acids), tri calcium phosphate, potassium citrate, potassium chloride, choline bitartrate, magnesium acetate, calcium glycerophosphate, sodium hydrogen phosphate, oil from Crypthecodinium cohnii, oil from Mortierella alpina, sodium chloride, inositol, L-ascorbic acid, antioxidants (sunflower lecithin, ascorbyl palmitate), ferrous sulphate, zinc sulphate, nicotinamide, DL-α-tocopheryl acetate, calcium D-pantothenate, copper sulphate, thiamin hydrochloride, pyridoxine hydrochloride, riboflavin, retinyl acetate, potassium iodide, manganese sulphate, pteroylmonoglutamic acid, chromium chloride, phytomenadione, sodium selenite, sodium molybdate, D-biotin, cholecalciferol, cyanocobalamin.
Allergens: N/A

Energivit
Powdered amino acid

L-Leucine, L-Valine, L-Isoleucine

To tailor nutritional intake to meet individual requirements.

Suitable for infants, children, and adults

L-Isoleucine: A powdered form of the amino acid L-Isoleucine. For use as a supplement in the dietary management of conditions requiring additional L-Isoleucine e.g., maple syrup urine disease.
L-Valine: A powdered form of the amino acid L-Valine. For use as a supplement in the dietary management of conditions requiring additional L-Valine e.g., maple syrup urine disease.
L-Leucine: A powdered form of the amino acid L-Leucine. For use as a supplement in the dietary management of conditions requiring additional L-Leucine e.g., maple syrup urine disease.

  • Suitable from birth to meet individual requirements.
  • A powdered form of the individual amino acids; either L-Isoleucine, L-Valine, or L-Leucine.
  • For use as a supplementary in the dietary management of MSUD as required
  • Available in a 100g tub

Ingredients: 
L-Leucine: L-Leucine,
L-Valine: L-Valine,
L-Isoleucine: L-Isoleucine
Allergens: N/A

Flavour sachets

To add variety and aid adherence for use in combination with our neutral flavoured powdered protein substitutes.

A Grapefruit flavoured powder consisting of a mixture of citric acid and flavouring. With sweetener.
A Lemon-Lime flavoured powder consisting of a mixture of citric acid, flavouring and colour. With sweetener.
A Cherry-Vanilla flavoured powder consisting of a mixture of malic acid, flavourings, and colour. With sugar and sweetener.

Suitable for use with a range of unflavoured amino acid and peptide-based foods for special medical purposes.

  • Offer variety with 3 ready to mix flavours: Cherry-Vanilla, Lemon-Lime and Grapefruit.
  • Available in a box of 20 x 5g sachets.
  • Contains a carbohydrate base with sugars and sweeteners.

Ingredients: 
Grapefruit flavour: Flavour enhancer (citric acid), flavouring (32%), sweetener (acesulfame-K).
Lemon-Lime flavour: Flavour enhancer (citric acid), flavouring (31%), sweetener (acesulfame-K), colour (carotenes).
Cherry-Vanilla flavour: Flavourings (40%), flavour enhancer (malic acid), colour (betanin), glucose syrup, sweetener (acesulfame-K).
Allergens: N/A

Flavour sachets
Loprofin range

Loprofin Range

Low protein kitchen essentials that can be used in any rare disorder of protein metabolism to provide additional energy and increase variety and flavour in low-protein diets.

Combine Loprofin kitchen essentials with local and globally created recipes to prepare tasty meals and snacks from breakfast to dinner.

Find out more

Inherited Metabolic Disorders

Inherited metabolic disorders (IMDs), also known as Inborn errors of metabolism (IEM) are a group of rare disorders caused by genetic defects.

Find out more

Learn more about latest research

News article about recent systematic review and meta-analysis exploring why protein substitutes are still very relevant to patients with PKU on BH4 treatment.

Find out more

* A blend researched and designed by Nutricia as part of the development of nutrition for healthy infants and similar to oligosaccharides in breast milk.
* As compared to other iFSMPs in the UK market, MIMS Nov 2020
** Nutricia products are manufactured to conform with food industry good manufacturing practices as described in the FSSC 22000 standard
*** Taste testing carried out with patients with IMD, data on file; 2017

  1. Moro G and Boehm H. Functional Food Review 2012; 4:1-12 - as compared to other iFSMPs in the UK market, MIMS Nov 2020
  2. Trier E et al. JPGN 1999;28(5):595
  3. Evans S et al. J Hum Nutr Diet 2009;22:414-421
  4. Hofman Z et al. Clin Nutr 2001;20(S3)217A:P63
  5. Daly A et al. J Hum Nutr Diet 2004;17:365–70.
  6. Guimber D et al. J Pediatr Gastroenterol Nutr 2007;44e201 (PN1–15).
  7. Grogan J et al. J Hum Nutr Diet 2006; 19:458–477
  8. Scientific Advisory Committee on Nutrition, Advice on fish consumption: benefits and risks, 2004, The Stationary Office: London
  9. Vilaseca MA et al., Long-chain polyunsaturated fatty acid concentration in patients with inborn errors of metabolism. Nutrición Hospitalaria, 2011. 26: p.128-136
  10. Verkerk PH, Twintig jaar landelijke screening op fenylketonurie in Nederland. Ned Tijdschr Geneeskd, 1995. 139; p.2302-5
  11. Van Vliet K et al. Nutrients. 2019 Aug 27;11(9):2011

Are you a healthcare professional or (carer of) a diagnosed patient?

The product information for this area of specialization is intended for healthcare professionals or (carers of) diagnosed patients only, as these products are for use under healthcare professional supervision.

Please click ‘Yes’ if you are a healthcare professional or (carer of) a diagnosed patient, or ‘No’ to be taken to a full list of our products.

No

The information on this page is intended for healthcare professionals only.

If you aren't a healthcare professional, you can visit the page with general information, by clicking 'I'm not a healthcare professional' below.

x